{"id":11,"date":"2026-10-15T13:57:56","date_gmt":"2026-10-15T13:57:56","guid":{"rendered":"http:\/\/pedirom.org.tr\/index.php\/ailevi-akdeniz-atesi-fmf\/"},"modified":"2026-10-15T13:57:56","modified_gmt":"2026-10-15T13:57:56","slug":"ailevi-akdeniz-atesi-fmf","status":"publish","type":"page","link":"https:\/\/pedirom.org.tr\/index.php\/ailevi-akdeniz-atesi-fmf\/","title":{"rendered":"Ailevi Akdeniz Ate\u015fi (FMF)"},"content":{"rendered":"<figure class=\"pr-fig\"><img loading=\"lazy\" decoding=\"async\" src=\"http:\/\/pedirom.org.tr\/wp-content\/themes\/cocuk-romatoloji-rehberi\/assets\/img\/ailevi-akdeniz-atesi-fmf.jpg\" alt=\"Ailevi Akdeniz Ate\u015fi (FMF) \u2013 temsil\u00ee ill\u00fcstrasyon\" width=\"1200\" height=\"750\"><figcaption>Temsil\u00ee ill\u00fcstrasyon<\/figcaption><\/figure>\n<p>Ailevi Akdeniz Ate\u015fi, k\u0131saca FMF, tekrarlayan ate\u015f ve iltihap ataklar\u0131 ile seyreden kal\u0131tsal bir hastal\u0131kt\u0131r. T\u00fcrkiye, FMF\u2019nin en s\u0131k g\u00f6r\u00fcld\u00fc\u011f\u00fc \u00fclkeler aras\u0131ndad\u0131r. Hastal\u0131k genellikle \u00e7ocukluk \u00e7a\u011f\u0131nda ba\u015flar.<\/p>\n<h2>Kal\u0131t\u0131m<\/h2>\n<p>FMF, MEFV adl\u0131 gendeki de\u011fi\u015fikliklerle ili\u015fkilidir ve \u00e7o\u011funlukla \u00e7ekinik kal\u0131t\u0131mla aktar\u0131l\u0131r. \u00dclkemizde bu gende de\u011fi\u015fiklik ta\u015f\u0131yan ama hasta olmayan \u00e7ok say\u0131da ki\u015fi bulunur. Genetik testin yorumu bu nedenle dikkat gerektirir; ayr\u0131nt\u0131lar <a href=\"http:\/\/pedirom.org.tr\/index.php\/mefv-gen-testi\/\">MEFV gen testi<\/a> sayfam\u0131zda.<\/p>\n<h2>Ataklar<\/h2>\n<p>Tipik atak, genellikle yar\u0131m g\u00fcnle \u00fc\u00e7 g\u00fcn aras\u0131nda s\u00fcren ate\u015fe e\u015flik eden \u015fiddetli kar\u0131n a\u011fr\u0131s\u0131yla seyreder. G\u00f6\u011f\u00fcs a\u011fr\u0131s\u0131, eklem a\u011fr\u0131s\u0131 ve \u015fi\u015fli\u011fi, \u00f6zellikle bileklerde k\u0131zar\u0131k ve a\u011fr\u0131l\u0131 d\u00f6k\u00fcnt\u00fc ve kas a\u011fr\u0131s\u0131 da g\u00f6r\u00fclebilir. Ataklar aras\u0131nda \u00e7ocuk genellikle tamamen sa\u011fl\u0131kl\u0131d\u0131r. \u015eiddetli kar\u0131n a\u011fr\u0131s\u0131 nedeniyle apandisit ile kar\u0131\u015fabilir.<\/p>\n<h2>Tan\u0131<\/h2>\n<p>Tan\u0131, ataklar\u0131n \u00f6zelliklerine, muayene bulgular\u0131na, atak s\u0131ras\u0131nda y\u00fckselen iltihap g\u00f6stergelerine ve tedaviye yan\u0131ta dayan\u0131r. Genetik test tan\u0131y\u0131 destekleyebilir; ancak tek ba\u015f\u0131na tan\u0131 koydurmaz ya da d\u0131\u015flamaz.<\/p>\n<h2>Tedavi ve amiloidoz<\/h2>\n<p>FMF\u2019de temel tedavi, hekimin \u00f6nerdi\u011fi \u015fekilde d\u00fczenli kullan\u0131lan kol\u015fisindir. Tedavinin amac\u0131 yaln\u0131zca ataklar\u0131 azaltmak de\u011fil, tedavi edilmeyen hastalarda b\u00f6brekleri etkileyebilen amiloidoz adl\u0131 ciddi komplikasyonu \u00f6nlemektir. Kol\u015fisin hekim \u00f6nerisi olmadan b\u0131rak\u0131lmamal\u0131 ya da dozu de\u011fi\u015ftirilmemelidir. Kol\u015fisine yan\u0131t vermeyen ya da tolere edemeyen hastalarda ba\u015fka tedaviler de\u011ferlendirilir.<\/p>\n<h2>Takip<\/h2>\n<p>D\u00fczenli kontrollerde atak s\u0131kl\u0131\u011f\u0131, b\u00fcy\u00fcme, idrarda protein ve kan de\u011ferleri izlenir. Atak s\u0131ras\u0131nda dayan\u0131lmaz kar\u0131n a\u011fr\u0131s\u0131, kusma ve genel durum bozuklu\u011fu olursa acil de\u011ferlendirme gerekir. Benzer ate\u015f tablolar\u0131 i\u00e7in <a href=\"http:\/\/pedirom.org.tr\/index.php\/pfapa-periyodik-ates\/\">PFAPA ve periyodik ate\u015f sendromlar\u0131<\/a> sayfam\u0131za bakabilirsiniz.<\/p>\n<p class=\"kaynak\"><small>Genel bilgi kaynaklar\u0131: EULAR (Avrupa Romatoloji Birli\u011fi) \u00f6nerileri \u2013 FMF y\u00f6netimi (2016); T\u00fcrk pediatrik FMF tan\u0131 \u00f6l\u00e7\u00fctleri (Yal\u00e7\u0131nkaya-\u00d6zen); Avrupa Pediatrik Romatoloji Derne\u011fi (PRES) ve SHARE giri\u015fimi \u00f6nerileri. Kontrol tarihi: Ekim 2026. Bu sayfa hekim incelemesinden ge\u00e7mi\u015f bir t\u0131bbi metin de\u011fildir; tan\u0131 ve tedavi i\u00e7in \u00e7ocu\u011funuzun hekimine ba\u015fvurun. Acil durumda 112\u2019yi aray\u0131n.<\/small><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Ailevi Akdeniz Ate\u015fi (FMF): kal\u0131t\u0131m, ate\u015f ve kar\u0131n a\u011fr\u0131s\u0131 ataklar\u0131, tan\u0131n\u0131n nas\u0131l kondu\u011fu, kol\u015fisin tedavisinin \u00f6nemi, amiloidoz riski ve takip.<\/p>\n","protected":false},"author":0,"featured_media":0,"parent":0,"menu_order":4,"comment_status":"closed","ping_status":"closed","template":"","meta":{"footnotes":""},"class_list":["post-11","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/pedirom.org.tr\/index.php\/wp-json\/wp\/v2\/pages\/11","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/pedirom.org.tr\/index.php\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/pedirom.org.tr\/index.php\/wp-json\/wp\/v2\/types\/page"}],"replies":[{"embeddable":true,"href":"https:\/\/pedirom.org.tr\/index.php\/wp-json\/wp\/v2\/comments?post=11"}],"version-history":[{"count":2,"href":"https:\/\/pedirom.org.tr\/index.php\/wp-json\/wp\/v2\/pages\/11\/revisions"}],"predecessor-version":[{"id":51,"href":"https:\/\/pedirom.org.tr\/index.php\/wp-json\/wp\/v2\/pages\/11\/revisions\/51"}],"wp:attachment":[{"href":"https:\/\/pedirom.org.tr\/index.php\/wp-json\/wp\/v2\/media?parent=11"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}